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Diagnosis and management of idiopathic pulmonary fibrosis: French practical guidelines.

Vincent Cottin 1, 2, 3 Bruno Crestani 4 Dominique Valeyre 5 Benoit Wallaert 6 Jacques Cadranel 7 Jean-Charles Dalphin 8 Philippe Delaval 9 Dominique Israel-Biet 10 Romain Kessler 11 Martine Reynaud-Gaubert 12 Bernard Aguilaniu 13 Benoit Bouquillon 14 Philippe Carré 15 Claire Danel 4 Jean-Baptiste Faivre 16 Gilbert Ferretti 17 Nicolas Just 18 Serge Kouzan 19 François Lebargy 20 Sylvain Marchand-Adam 21, 22 Bruno Philippe 23 Grégoire Prévot 24 Bruno Stach Françoise Thivolet-Béjui 25 Jean-François Cordier 25 
Abstract : Idiopathic pulmonary fibrosis (IPF) is the most frequent chronic idiopathic interstitial pneumonia in adults. The management of rare diseases in France has been organised by a national plan for rare diseases, which endorsed a network of expert centres for rare diseases throughout France. This article is an overview of the executive summary of the French guidelines for the management of IPF, an initiative that emanated from the French National Reference Centre and the Network of Regional Competence Centres for Rare Lung Diseases. This review aims at providing pulmonologists with a document that: 1) combines the current available evidence; 2) reviews practical modalities of diagnosis and management of IPF; and 3) is adapted to everyday medical practice. The French practical guidelines result from the combined efforts of a coordination committee, a writing committee and a multidisciplinary review panel, following recommendations from the Haute Autorité de Santé. All recommendations included in this article received at least 90% agreement by the reviewing panel. Herein, we summarise the main conclusions and practical recommendations of the French guidelines.
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Submitted on : Friday, June 17, 2022 - 11:05:03 AM
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Vincent Cottin, Bruno Crestani, Dominique Valeyre, Benoit Wallaert, Jacques Cadranel, et al.. Diagnosis and management of idiopathic pulmonary fibrosis: French practical guidelines.. European Respiratory Review, European Respiratory Society, 2014, 23 (132), pp.193-214. ⟨10.1183/09059180.00001814⟩. ⟨hal-01063982⟩



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